Tuberous Sclerosis is a rare congenital disease of neuroectodermal origin, inherited as AD, and known as Bourneville´s disease of Epiloia.
This lesion has clinical triad of mental retardation, seizure and adenoma sebacevm, and associated hamartoma or cyst is found at any organ, especially at brain, skin and kindey.
In brain, hamartomas are found largely at cerebrum and more specifically at subependymal layer of ventricle, especially near the foramen of Monro.
Authors experienced 2 cases of Tuberous Sclerosis, who have typical clinical symptomes and Computed Tomographic findings of brain and kidney, and reported with a brief review of the literatures.
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